Dyke-Davidoff-Masson syndrome is a rare syndrome with characteristic cerebral hemiatrophy/hypoplasia, contralateral hemiparesis, seizures, and compensatory osseous hypertrophy

doi:10.5083/ejcm/2023

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Research Article | Volume 13 Issue:4 (, 2023) | Pages 1355 - 1356

Dyke-Davidoff-Masson syndrome is a rare syndrome with characteristic cerebral hemiatrophy/hypoplasia, contralateral hemiparesis, seizures, and compensatory osseous hypertrophy

Dr Devina Singh, and Dr Navneet Kaur

MD Paediatrics, Senior Resident, Department of Paediatrics, Government Medical College, Patiala

Under a Creative Commons license

Open Access

DOI : 10.5083/ejcm/2023

Received

Oct. 1, 2023

Revised

Nov. 7, 2023

Accepted

Dec. 1, 2023

Published

Dec. 26, 2023

Abstract

Background: Dyke-Davidoff-Masson syndrome is a rare condition resulting from brain injury due to a multitude of causes; especially in early life. Characteristics include cerebral hemiatrophy/hypoplasia, contralateral hemiparesis, seizures, and compensatory osseous hypertrophy. Case presentation: We present a case of a 14-year-old girl who initially presented with left sided hemiparesis. Computed tomography (CT) showed evidence of right cerebral atrophy. Workup for paediatric stroke was negative. Upon further evaluation by Neuroradiology, features suggesting Dyke-Davidoff-Masson syndrome were confirmed. Patient has been under Neurology follow up since. Conclusions: Due to its rarity, Dyke-Davidoff-Masson syndrome may easily be missed by the majority of treating clinicians. Knowledge of its features on imaging enables timely and accurate diagnosis – allowing appropriate management.

Keywords

Dyke – Davidoff – Masson Syndrome

Computed

European Journal of Cardiovascular Medicine

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